Rare bone disorder affecting the temporal bone

Area of Science:

• Otolaryngology
• Pathology
• Radiology

Background:

• Fibrous dysplasia is a rare, benign bone disorder of unknown cause.
• It typically affects multiple bones but can present in a single bone (monostotic).
• Isolated involvement of the temporal bone is exceptionally uncommon.

Observation:

• This report describes three distinct cases of monostotic fibrous dysplasia.
• Each case uniquely featured extensive involvement of the entire temporal bone.
• Clinical and radiological findings were analyzed for each patient.

Findings:

• Monostotic fibrous dysplasia can present as a rare, isolated lesion of the temporal bone.
• The disorder demonstrated capacity for complete temporal bone infiltration in these cases.
• Diagnostic imaging is crucial for identifying the extent of temporal bone involvement.

Implications:

• Highlights the importance of considering fibrous dysplasia in the differential diagnosis of temporal bone lesions.
• Emphasizes the need for thorough radiological assessment to determine the full extent of the disease.
• Contributes to understanding the rare manifestations of fibrous dysplasia in the craniofacial skeleton.