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Situs anomalies and gastrointestinal abnormalities.
Seung Eun Lee1, Hyun-Young Kim, Sung-Eun Jung
1Department of Surgery, Seoul National University College of Medicine, Seoul 110-744, South Korea.
Journal of Pediatric Surgery
|July 5, 2006
Summary
Situs anomalies are frequently associated with gastrointestinal abnormalities, particularly in patients with right isomerism. Early imaging is recommended for patients with congenital heart disease or atypical organ positioning.
Area of Science:
- Pediatric Radiology
- Gastroenterology
- Medical Genetics
Background:
- Situs anomalies encompass a spectrum of conditions affecting organ laterality.
- These anomalies can range from isolated findings to complex syndromes.
- Gastrointestinal complications are a significant concern in patients with situs anomalies.
Purpose of the Study:
- To review gastrointestinal abnormalities associated with various types of situs anomalies.
- To identify the prevalence and types of intra-abdominal pathologies in pediatric patients with situs anomalies.
- To correlate specific situs anomalies with distinct gastrointestinal complications.
Main Methods:
- Retrospective analysis of pediatric patients diagnosed with situs anomalies.
- Inclusion criteria: Patients from Seoul National University Children's Hospital (1980-2004).
- Diagnostic modalities included echocardiography, angiography, ultrasonography, CT, and upper gastrointestinal studies.
Main Results:
- 67 patients with situs anomalies were identified: 45 situs inversus, 16 right isomerism, 6 left isomerism.
- High prevalence of intra-abdominal abnormalities: 58% in situs inversus, 88% in right isomerism, 67% in left isomerism.
- Common abnormalities included duodenal atresia, biliary atresia, malrotation, hiatal hernia, and diaphragmatic hernia.
Conclusions:
- Gastrointestinal abnormalities are common in pediatric patients with situs anomalies.
- Right isomerism showed the highest association with intra-abdominal pathologies.
- Recommended imaging includes chest radiography, abdominal ultrasonography, upper GI study, and CT for suspected cases.