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Diffuse supravalvular aortic stenosis: comprehensive imaging with ECG-gated CT angiography

Peter S Liu1, Martin G St John Sutton, Harold I Litt

  • 1Department of Radiology, University of Pennsylvania School of Medicine, 3400 Spruce Street, Philadelphia, PA 19104, USA.

Summary

Congenital supravalvular aortic stenosis (SVAS) is a rare condition causing left ventricular outflow obstruction. ECG-gated multidetector CT is effective for diagnosing diffuse SVAS and assessing disease extent.

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