Elderly manifestation of non-compaction of the ventricular myocardium

Altin Palloshi1, Patrizia Puccetti, Gabriele Fragasso

  • 1Cardio-Thoracic Department, Istituto Scientifico San Raffaele and Vita-Salute University, Milan, Italy. Altin_p@hotmail.com

Insights

Non-compaction of the ventricular myocardium (NCVM) is a rare heart condition. This report details an elderly patient, highlighting NCVM

Area of Science:

  • Cardiology
  • Genetics
  • Pathology

Background:

  • Non-compaction of the ventricular myocardium (NCVM) is a rare congenital heart defect.
  • It is typically diagnosed in childhood and associated with significant mortality.
  • NCVM in elderly individuals is exceptionally rare, with few documented cases.

Observation:

  • A case of a 74-year-old male with left ventricular NCVM is presented.
  • This represents one of the oldest reported patients with this condition.
  • The patient experienced a late onset of NCVM symptoms and rapid clinical decline.

Findings:

  • The case highlights NCVM in an advanced geriatric patient.
  • Late-onset NCVM with rapid deterioration was observed.
  • The patient's presentation challenges typical NCVM diagnostic timelines.

Implications:

  • This case expands the known age spectrum for NCVM diagnosis.
  • It supports the theory that NCVM may be multifactorial, not solely congenital.
  • Further research into the diverse etiology and presentation of NCVM is warranted.

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