Coarctation of the aorta in the right aortic arch with left aberrant innominate artery

Shelli Bein1, Ziad Saba, Hitendra Patel

  • 1Columbia University Medical Center, Medical School for International Health, New York, NY 10032, USA. shelliyaelbein@yahoo.com

Pediatric Cardiology
|August 26, 2006
PubMed

Insights

A rare combination of right aortic arch and aberrant left innominate artery was found with coarctation of the aorta. This unique case highlights the development and management of aortic arch anomalies and coarctation.

Area of Science:

  • Cardiovascular surgery
  • Congenital heart disease
  • Vascular anatomy

Background:

  • Right aortic arch is a rare congenital anomaly.
  • Aberrant left innominate artery is a variation in aortic arch branching.
  • Coarctation of the aorta is a narrowing of the aortic arch.

Observation:

  • A unique case of coarctation of the aorta is presented.
  • The patient had a right aortic arch and an aberrant left innominate artery.
  • A diverticulum of Kommerell gave rise to the left innominate artery and left ligamentum arteriosum, forming a vascular ring.

Findings:

  • This combination of anomalies is exceptionally rare.
  • The presence of a right aortic arch and aberrant left innominate artery complicates the vascular anatomy.
  • The diverticulum of Kommerell's role in forming the vascular ring is detailed.

Implications:

  • This case provides insights into the embryological development of complex aortic arch anomalies.
  • It raises questions about the pathogenesis of coarctation in the context of a right-sided aortic arch.
  • Management strategies for patients with this rare combination require careful consideration.

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