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[Embryonal rhabdomyosarcoma diagnosed antenatally]
B Pautard1, J P Canarelli, M F Gontier
1I'Unité d'Hématologie Oncologie Infantile, CHRU Amiens.
Archives Francaises De Pediatrie
|June 1, 1990
Summary
Congenital embryonal rhabdomyosarcoma in a newborn was diagnosed via ultrasound. Despite initial treatment and recurrence, the child is healthy after surgery and chemotherapy.
Area of Science:
- Pediatric Oncology
- Skeletal Muscle Tumors
- Congenital Malformations
Background:
- Congenital embryonal rhabdomyosarcoma is a rare pediatric malignancy.
- Maternal history of sterility and diagnosis via prenatal echography are notable factors.
- The case highlights challenges in managing rare congenital tumors.
Observation:
- Diagnosis of a large right shoulder tumor via echography at 36 weeks gestation.
- Cesarean section delivery necessitated due to tumor size.
- Postnatal assessment confirmed congenital embryonal rhabdomyosarcoma.
Findings:
- Initial surgical treatment followed by VAC chemotherapy.
- Local recurrence observed after 4 courses of VAC chemotherapy.
- Successful management through second surgical excision and IVA chemotherapy.
Implications:
- Demonstrates the feasibility of multimodal treatment for congenital rhabdomyosarcoma.
- Highlights the importance of prenatal diagnosis and timely intervention.
- Suggests potential for favorable outcomes with aggressive management strategies.