The presentation and management of vascular rings: an otolaryngology perspective

Rahul K Shah1, Bassem N Mora, Emile Bacha

  • 1Division of Otolaryngology, Children's National Medical Center, 111 Michigan Avenue, NW, Washington, DC 20010, USA. reza.rahbar@childrens.harvard.edu

Insights

Vascular rings in children commonly cause airway and feeding problems. Early diagnosis with imaging and bronchoscopy guides surgical release, with minimally invasive options available.

Area of Science:

  • Pediatric Surgery
  • Cardiovascular Surgery
  • Thoracic Surgery

Background:

  • Vascular rings are congenital anomalies where the great arteries form a ring around the trachea and esophagus.
  • These anomalies can lead to significant respiratory and feeding difficulties in infants and children.

Purpose of the Study:

  • To review the clinical presentation and natural history of pediatric patients diagnosed with vascular rings.
  • To establish management guidelines for children with vascular rings.

Main Methods:

  • Retrospective chart review of patients diagnosed with vascular rings at a tertiary care pediatric medical center.
  • Data collected from 1991 to 2002, including patient demographics, symptoms, diagnostic studies, and surgical interventions.

Main Results:

  • 37 males and 27 females were diagnosed with vascular rings.
  • 91% of patients presented with airway symptoms (e.g., stridor, recurrent infections) and 47% with esophageal symptoms (e.g., dysphagia).
  • Common diagnostic tools included echocardiography (96%), chest X-ray (93%), and barium swallow (75%). Surgical management involved open (n=25) and thoracoscopic (n=39) approaches, with an 8% rate of recurrent laryngeal nerve injury.

Conclusions:

  • Children with vascular rings typically present with respiratory and/or feeding issues.
  • Diagnostic workup should involve chest X-ray, echocardiography, barium swallow, and direct laryngoscopy/bronchoscopy.
  • Surgical intervention is indicated upon diagnosis, with both open and minimally invasive (thoracoscopic, robotic-assisted) options available.
Abstract

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