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Published on: July 5, 2021
Sinus node dysfunction in a patient with left atrial isomerism.
Sírio Hassem Sobrinho1, Airton Camacho Moscardini, Ulisses Alexandre Croti
1Faculdade de Medicina de São José do Rio Preto, São José do Rio Preto, SP, Brazil. siriohassem@cardiol.br
A child with left atrial isomerism and a sinus venosus atrial septal defect experienced bradycardia due to sinus node dysfunction. A pacemaker implantation resolved the issue, ensuring a satisfactory outcome.
Area of Science:
- Pediatric Cardiology
- Congenital Heart Disease
Background:
- Left atrial isomerism is a rare congenital anomaly.
- Sinus venosus atrial septal defects are a subset of atrial septal defects.
Observation:
- An asymptomatic six-year-old child presented with bradycardia.
- Electrocardiographic monitoring revealed significant sinus node dysfunction with prolonged sinus pauses.
Findings:
- The patient had left atrial isomerism and a sinus venosus atrial septal defect.
- Sinus node dysfunction was confirmed with pauses up to 2.4 seconds.
Implications:
- Early detection and management of sinus node dysfunction in children with congenital heart disease are crucial.
- Pacemaker implantation can be an effective treatment for symptomatic sinus node dysfunction in this population.
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