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Updated: Jul 18, 2026

Scanning Electron Microscopy of Macerated Tissue to Visualize the Extracellular Matrix
10:21

Scanning Electron Microscopy of Macerated Tissue to Visualize the Extracellular Matrix

Published on: June 14, 2016

Extracellular matrix turnover and disease severity in Anderson-Fabry disease

J S Shah1, D A Hughes, M H Tayebjee

  • 1The Heart Hospital, UCL, London, UK.

Journal of Inherited Metabolic Disease
|December 13, 2006
PubMed
Summary

Anderson-Fabry Disease (AFD) involves abnormal extracellular matrix (ECM) turnover, indicated by elevated matrix metalloproteinase-9 (MMP-9) levels. Higher MMP-9 correlates with disease severity and impaired heart function in AFD patients.

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