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Autosomal dominant inherence of multiple supernumerary teeth
1Department of Oral and Maxillofacial Surgery, Shandong University School of Stomatology, Jinan, Shandong, People's Republic of China.
International Journal of Oral and Maxillofacial Surgery
|March 21, 2007
Summary
This case study highlights a rare instance of 16 supernumerary teeth in a young female patient with congenital heart disease. Genetic factors are suggested as a significant influence on this dental anomaly, supported by family history.
Area of Science:
- Dentistry
- Genetics
- Pediatrics
Background:
- Supernumerary teeth, also known as hyperdontia, are a relatively common dental anomaly.
- Congenital cardiopathy is a structural defect of the heart present at birth.
- The etiology of supernumerary teeth is often multifactorial, involving genetic and environmental influences.
Observation:
- An 11-year-old Chinese female patient presented with 16 supernumerary teeth.
- The patient also had a diagnosis of congenital cardiopathy.
- The patient's mother exhibited the same clinical manifestation of supernumerary teeth.
Findings:
- A detailed family history investigation was conducted.
- The presence of multiple supernumerary teeth in a patient with congenital cardiopathy is a notable clinical observation.
- A familial pattern of supernumerary teeth was identified.
Implications:
- This case underscores the potential genetic basis for supernumerary teeth, particularly in syndromic cases.
- Further research into the genetic underpinnings of dental anomalies and their association with systemic conditions is warranted.
- Understanding genetic factors can aid in early diagnosis and management of dental anomalies.
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