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Long-term outcome in a patient with pulmonary hypertension and hereditary hemorrhagic telangiectasia

Omar A Minai1, Christina Rigelsky, Charis Eng

  • 1Department of Pulmonary, Allergy, and Critical Care Medicine, A90, Cleveland Clinic, 9500 Euclid Ave, Cleveland, OH 44195, USA. minaio@ccf.org

Chest
|April 12, 2007
PubMed

Hereditary hemorrhagic telangiectasia (HHT) may be associated with pulmonary hypertension (PH). In the context that little attention has been given to long-term follow-up of such individuals, we report a patient with PH associated with HHT with special attention to clinical features and long-term response to therapy. To our knowledge, this case represents only the second with a 10-year follow-up reported and demonstrates that aggressive therapy can lead to long-term improvement in clinical parameters and survival.

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