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Linear morphea presenting as acquired unilateral edema.
Katherine H Fiala1, Michael J Wells, Kimberly A Mullinax
1Department of Dermatology, Texas Tech University Health Sciences Center, Lubbock, Texas, USA.
Pediatric Dermatology
|April 28, 2007
Summary
Bullous morphea, a rare condition, presented as unilateral edema and bullae in a child. This case highlights its association with lymphedema, expanding differential diagnoses for pediatric edema.
Area of Science:
- Dermatology
- Pediatrics
- Pathology
Background:
- Morphea is a connective tissue disease characterized by localized sclerotic skin lesions.
- Acquired unilateral edema in children can have various etiologies, necessitating a broad differential diagnosis.
Observation:
- A 2-year-old boy presented with progressive unilateral edema, bullae, and linear hypopigmented patches.
- The lesions evolved to indurated, bound-down patches, particularly over the left groin and thigh.
- Biopsy confirmed features consistent with morphea.
Findings:
- The patient's morphea led to sclerosis and dilation of lymphatic channels, causing bullae formation.
- This presentation represents bullous morphea with associated lymphedema.
- No prior reports documented bullous morphea in individuals under 18 with lymphedema.
Implications:
- Bullous morphea should be considered in the differential diagnosis of acquired unilateral edema in pediatric patients.
- This case expands the understanding of morphea's rare presentations and complications in children.
- Early recognition is crucial for appropriate management of pediatric lymphedema and morphea.
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