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Anetodermic mastocytosis: response to PUVA therapy.
Jesús Del Pozo1, María Teresa Yebra Pimentel, Sabela Paradela
1Department of Dermatology, Hospital Juan Canalejo, La Coruña, Spain. del_pozo@canalejo.org
The Journal of Dermatological Treatment
|June 1, 2007
Summary
Anetodermic mastocytosis, a rare skin condition, presents with unusual lesions. Early investigation of Darier's sign in unclear anetodermic lesions can help diagnose cutaneous mastocytosis.
Area of Science:
- Dermatology
- Hematology
Background:
- Mastocytosis is a rare disorder involving mast cell accumulation in various organs.
- Cutaneous involvement is common, presenting diverse clinical manifestations.
- Anetodermic lesions represent an uncommon clinical presentation of mastocytosis.
Observation:
- A 26-year-old male presented with sparse anetodermic lesions.
- The patient experienced a benign clinical course.
- PUVA (psoralen plus ultraviolet A) therapy was administered.
Findings:
- Anetodermic mastocytosis was diagnosed in the patient.
- The condition followed a benign clinical course.
- PUVA therapy demonstrated excellent therapeutic results.
Implications:
- Darier's sign warrants investigation in patients with unexplained anetodermic lesions.
- This approach aids in the exclusion of cutaneous mastocytosis.
- Recognizing this rare presentation is crucial for timely diagnosis and management.