Right coronary artery fistula draining into the right atrium and associated with mitral valve stenosis: a case report

Ali Gürbüz1, Ufuk Yetkin, Omer Tetik

  • 1Izmir Atatürk Education and Research Hospital, Department of Cardiovascular Surgery, Izmir, Turkey.

Insights

Coronary artery fistula (CAF), a rare congenital anomaly, can coexist with mitral stenosis. Surgical repair of CAF is recommended to prevent complications and improve patient quality of life.

Area of Science:

  • Cardiology
  • Congenital Heart Disease
  • Interventional Cardiology

Background:

  • Coronary artery fistula (CAF) is a rare congenital anomaly with an incidence of 1 in 50,000 live births.
  • Coexistence of CAF and mitral stenosis is infrequently reported in medical literature.
  • CAF involves abnormal connections between coronary arteries and cardiac chambers or major vessels.

Observation:

  • A rare case of CAF with mitral valve stenosis presented with dyspnea and fatigue.
  • Coronary angiography revealed a fistula connecting the right coronary artery to the right atrium.
  • A fistula draining into the right atrium is uncommon in patients with coronary artery anomalies and mitral valve disease.

Findings:

  • The patient underwent surgical repair of the CAF and radiofrequency ablation.
  • Post-surgical coronary angiography confirmed normal coronary anatomy and fistula occlusion.
  • CAF diagnosis may be enhanced by simultaneous coronary angiography during cardiac catheterization for valve evaluation.

Implications:

  • Early diagnosis and surgical repair of CAF are crucial for preventing complications.
  • Surgical intervention improves the quality of life for patients with CAF.
  • Consideration of CAF in patients with valvular heart disease may improve diagnostic rates.

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