Right coronary artery fistula draining into the right atrium and associated with mitral valve stenosis: a case report
Ali Gürbüz1, Ufuk Yetkin, Omer Tetik
1Izmir Atatürk Education and Research Hospital, Department of Cardiovascular Surgery, Izmir, Turkey.
Insights
Coronary artery fistula (CAF), a rare congenital anomaly, can coexist with mitral stenosis. Surgical repair of CAF is recommended to prevent complications and improve patient quality of life.
Area of Science:
- Cardiology
- Congenital Heart Disease
- Interventional Cardiology
Background:
- Coronary artery fistula (CAF) is a rare congenital anomaly with an incidence of 1 in 50,000 live births.
- Coexistence of CAF and mitral stenosis is infrequently reported in medical literature.
- CAF involves abnormal connections between coronary arteries and cardiac chambers or major vessels.
Observation:
- A rare case of CAF with mitral valve stenosis presented with dyspnea and fatigue.
- Coronary angiography revealed a fistula connecting the right coronary artery to the right atrium.
- A fistula draining into the right atrium is uncommon in patients with coronary artery anomalies and mitral valve disease.
Findings:
- The patient underwent surgical repair of the CAF and radiofrequency ablation.
- Post-surgical coronary angiography confirmed normal coronary anatomy and fistula occlusion.
- CAF diagnosis may be enhanced by simultaneous coronary angiography during cardiac catheterization for valve evaluation.
Implications:
- Early diagnosis and surgical repair of CAF are crucial for preventing complications.
- Surgical intervention improves the quality of life for patients with CAF.
- Consideration of CAF in patients with valvular heart disease may improve diagnostic rates.
Abstract:
Coronary artery fistula (CAF) is a rare congenital anomaly of the coronary arteries in which abnormal connections are present between the coronary artery branch and the cardiac chambers or a major vessel. The incidence of CAF is estimated at 1 in 50,000 live births, and it is detected in approximately 0.2% of the adult population during coronary angiography. Reports of the coincidence of mitral stenosis and CAF are rare in the literature. We report a case of CAF and mitral valve stenosis in a patient with dyspnea and fatigue before valve replacement and surgical radiofrequency ablation. Coronary angiography showed a connection between the right coronary artery and right atrium. A fistula opening into the right atrium is rare in patients with coronary artery anomalies and mitral valve disease. Coronary angiography of the patient 1 month after surgical repair showed that the coronary anatomy was normal and the fistula was occluded. CAF can be diagnosed more frequently if coronary angiography is performed simultaneously with cardiac catheterization to evaluate valve functions or nonatherosclerotic myocardial ischemia in each valvular heart disease case. Surgical repair of CAF is the first-choice treatment to prevent complications and improve quality of life.
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