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Audiologic results in patients with Moebiüs sequence.
Silvana Griz1, Mariana Cabral, Graziela Azevedo
1Fonoaudióloga, Doutora em Psicologia Cognitiva, Universidade Federal de Pernambuco, Endereço: Av. Flor de Santana, 189/301 Parnamirim, Recife/PE CEP 52060-290, Brazil. sgriz@terra.com.br
International Journal of Pediatric Otorhinolaryngology
|July 21, 2007
Summary
Children with Moebiüs sequence often have normal hearing, but audiology evaluations are crucial. This study found no specific hearing loss pattern, with most participants having normal hearing levels.
Area of Science:
- Otolaryngology
- Pediatrics
- Genetics
Background:
- Moebiüs sequence is a rare congenital disorder with poorly understood audiological implications.
- Hearing status in individuals with Moebiüs sequence requires further investigation.
Purpose of the Study:
- To characterize the audiological findings in children and adolescents diagnosed with Moebiüs sequence.
Main Methods:
- A cohort of 17 children and adolescents (ages 3-13) underwent comprehensive audiological assessments.
- Evaluations included auditory instrumentation, pure tone audiometry, speech audiometry, tympanometry, and otoacoustic emissions.
Main Results:
- 75% of ears tested showed normal hearing levels.
- Various hearing loss types (conductive, sensorineural, mixed) were observed in a minority of participants.
- Otoacoustic emissions were present in over 70% of participants, suggesting preserved cochlear function in most.
Conclusions:
- There is no distinct audiological pattern associated with Moebiüs sequence.
- The majority of individuals with Moebiüs sequence exhibit normal hearing.
- Audiological assessment is essential for individuals with Moebiüs sequence, as hearing loss is not a universal finding.
