[Anomalous left main coronary artery with an inter-aorto-pulmonary trajectory: diagnostic value of 64-slice CT scan
1Radiologie pédiatrique, Université René Descartes, Paris 5, Hôpital Necker-Enfants Malades, Paris. phalla.ou@nck.ap-hop-paris.fr
Insights
An anomalous left coronary artery originating from the right sinus can cause sudden death in young adults. A CT scan effectively diagnosed this rare condition in a child experiencing exertional syncope and angina.
Area of Science:
- Cardiology
- Medical Imaging
- Pediatric Cardiology
Background:
- Anomalous left coronary artery from the right sinus of Valsalva with an interarterial course is a rare congenital anomaly.
- This malformation can lead to myocardial ischemia and sudden cardiac death, particularly in young individuals, due to compression between the aorta and pulmonary artery during exercise.
Observation:
- A 12-year-old child presented with exertional syncope and angina, indicative of myocardial ischemia.
- Diagnostic imaging revealed an anomalous left coronary artery arising from the right aortic sinus with an inter-aorto-pulmonary trajectory.
Findings:
- Computed Tomography (CT) scan with 3-D reconstruction confirmed the diagnosis of anomalous left coronary artery.
- The CT scan precisely delineated the aberrant coronary artery's trajectory and its anatomical relationship with the great vessels at the heart's base.
Implications:
- Cardiac CT is the preferred imaging modality for diagnosing congenital coronary anomalies and for preoperative planning.
- CT angiography offers superior visualization of coronary anatomy compared to echocardiography and conventional angiography in suspected cases.
Abstract:
Anomalous left coronary artery arising from the right sinus with an inter-aorto-pulmonary trajectory is a classical cause of sudden death and myocardial ischaemia in young adults. The mechanism is compression of the coronary during physiological dilatation of the great arteries on exercise. The authors report the case of a 12 year old child who had syncope on effort preceded by angina due to this malformation. The CT scan with 3-D reconstruction confirmed the diagnosis and the interarterial trajectory of the left coronary artery and the anatomical relationships with the vessels at the base of the heart. Cardiac CT scan is the investigation of choice for diagnosis and preoperative work-up of congenital coronary anomalies. In the authors' experience, the investigation is performed systematically when an anomalous coronary artery is suspected, in addition to echocardiography and instead of conventional coronary angiography.
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