Related Experiment Videos
Facial reconstruction consideration in rheumatic diseases
R F Mayro1, J B DeLozier, L A Whitaker
1University of Pennsylvania School of Dental Medicine, Philadelphia.
Rheumatic Diseases Clinics of North America
|November 1, 1991
Summary
Facial JRA, Romberg disease, and scleroderma management depends on disease severity and patient factors. Surgical reconstruction requires a quiescent disease state and careful planning for optimal outcomes.
Area of Science:
- Rheumatology
- Plastic Surgery
- Orthodontics
Background:
- Facial involvement is a significant concern in Juvenile Rheumatoid Arthritis (JRA), Romberg disease, and scleroderma.
- These conditions can lead to functional occlusal abnormalities and aesthetic deformities.
- Current management strategies require careful consideration of disease activity and patient-specific factors.
Purpose of the Study:
- To outline the principles for managing facial disfigurement in JRA, Romberg disease, and scleroderma.
- To discuss the role of a multidisciplinary team in addressing functional occlusal abnormalities.
- To provide guidance on the timing and techniques for surgical facial reconstruction.
Main Methods:
- Review of management strategies for facial involvement in JRA, Romberg disease, and scleroderma.
- Emphasis on a team-based approach involving orthodontics and orthognathic surgery.
- Discussion of surgical reconstruction timing and techniques, including grafts, flaps, and implants.
Main Results:
- Management is tailored to disease severity, age of onset, and disease duration.
- Orthodontics and orthognathic surgery are key for functional occlusal issues.
- Surgical reconstruction in scleroderma is recommended only after at least one year of disease quiescence.
Conclusions:
- A multidisciplinary approach is crucial for optimizing functional and aesthetic outcomes in facial JRA, Romberg disease, and scleroderma.
- Delayed surgical intervention until disease quiescence is vital, particularly in scleroderma.
- Further research is needed to identify ideal methods for facial skeletal and soft-tissue augmentation.