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Broncholithiasis in an immune compromised boy with disseminated Mycobacterium kansasii
I Cuppen1, W C M de Lange, S S N de Graaf
1Department of Pediatrics, Radboud University Nijmegen Medical Centre, Nijmegen, The Netherlands. I.Cuppen@cukz.umcn.nl
Insights
Broncholithiasis, a rare condition where calcified lymph nodes obstruct airways, is reported in a child. This case highlights a unique presentation of broncholithiasis in a pediatric patient with disseminated Mycobacterium kansasii infection.
Area of Science:
- Pediatric Pulmonology
- Infectious Diseases
- Hematology Oncology
Background:
- Broncholithiasis, characterized by calcified lymph nodes eroding into bronchi, is uncommon in children.
- The most frequent etiology of broncholithiasis is Mycobacterium tuberculosis infection.
Observation:
- A 14-year-old boy with disseminated Mycobacterium kansasii infection and myelodysplastic syndrome presented with cough and fever.
- Computed tomography and bronchoscopy revealed a large calcified mass eroding the right main bronchus.
Findings:
- The patient experienced hemoptysis and clinical deterioration, leading to the discovery of acute myeloid leukemic transformation of his myelodysplastic syndrome.
- Post-mortem examination confirmed a large broncholith originating from a calcified lymph node.
Implications:
- This case underscores the importance of considering broncholithiasis in pediatric patients with complex infections and hematologic disorders.
- It highlights a rare association between Mycobacterium kansasii, myelodysplastic syndrome, leukemic transformation, and broncholithiasis in a child.
- Further research into the pathogenesis and management of pediatric broncholithiasis is warranted.
Abstract:
A case of broncholithiasis in a child is reported. To our knowledge, it has not been reported in children. Broncholithiasis is a condition in which a peribronchial calcified lymph node erodes into or distorts an adjacent bronchus. Symptoms of broncholithiasis include cough, recurrent episodes of fever, haemoptysis, and purulent sputum. The most common cause of broncholithiasis is Mycobacterium tuberculosis (M. tuberculosis). Here we describe a 14-year-old boy known to have disseminated Mycobacterium kansasii (M. kansasii) infection associated with hypoplastic myelodysplastic syndrome (MDS). He was presented with cough and fever. Computed tomography (CT) and bronchoscopy revealed a large calcified mass eroding in the right main bronchus. While surgical therapy was considered, haemoptysis developed and his condition deteriorated. Bone marrow puncture revealed acute myeloid leukemic transformation of the MDS. Curation was no longer possible. Post mortem examination revealed a large bronchiolith, evolving from a calcified lymph node.
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