[Hereditary angioedema. Description of a pediatric case]

Hereditary angioedema is a disease due to deficiency or functional anomaly of the serum inhibitor of C1-esterase, clinically characterised by the recurrence of oedematous episodes in the subcutis and mucosas; if not diagnoses in time, this condition is potentially fatal (up to 50% of cases for edema of the glottis). A case diagnosed in paediatric age is reported.