[Variant Brugada syndrome--mild ST segment elevation in inferior leads and aborted sudden cardiac death]

Piotr Kukla1, Marek Jastrzebski, Bogumiła Bacior

  • 1Oddział Wewnetrzny, Szpital Specjalistyczny im. H. Klimontowicza, Gorlice.

Kardiologia Polska
|January 9, 2008
PubMed

Insights

A man survived sudden cardiac death (SCD) due to variant Brugada syndrome. Persistent ST segment elevations in inferior leads may indicate this condition, even with negative cardiac markers.

Area of Science:

  • Cardiology
  • Electrophysiology
  • Genetics

Background:

  • Sudden cardiac death (SCD) is a critical condition requiring accurate diagnosis.
  • Variant Brugada syndrome is an inherited arrhythmia syndrome.
  • ST segment elevation in ECG can mimic acute coronary syndrome.

Observation:

  • A 48-year-old man survived aborted SCD with inferior ST segment elevation.
  • Initial investigations for acute coronary syndrome were negative.
  • Electrophysiological study and ajmaline test were positive for Brugada syndrome.

Findings:

  • The patient was diagnosed with variant Brugada syndrome.
  • Persistent inferior ST segment elevation was a key diagnostic feature.
  • A prolonged PQ interval and family history of SCD were noted.

Implications:

  • Persistent ST segment elevation in inferior leads may be a marker for variant Brugada syndrome.
  • This case highlights the importance of considering Brugada syndrome in unexplained SCD.
  • Early diagnosis and management are crucial for preventing future cardiac events.

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