Undifferentiated liver sarcoma -- rare entity: a case report and review of the literature
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Kashif Iqbal1, Zhang Meng Xian, Chen Yuan
1Nuclear Medicine, Oncology and Radiotherapy Institute, Islamabad, Pakistan. kashifrajput@yahoo.com
Introduction:
Undifferentiated Liver Sarcoma, also known as Undifferentiated Embryonal Sarcoma of the Liver, is a rare, highly malignant neoplasm which affects mostly the pediatric population, although a few cases have been reported in adults. It accounts for about 13% of pediatric hepatic malignancies.
Case Presentation:
We report a case of undifferentiated liver sarcoma in a 14-year-old Chinese boy who presented with non-specific right hypochondriac pain. Exploratory laparotomy with tumor resection was performed, followed by adjuvant chemotherapy.
Conclusion:
Undifferentiated Liver Sarcoma is a rare, highly malignant hepatic neoplasm affecting almost exclusively the pediatric population. The prognosis is poor but recent evidence shows that long-term survival is possible after complete surgical resection and postoperative chemotherapy.