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A Metadata Extraction Approach for Clinical Case Reports to Enable Advanced Understanding of Biomedical Concepts
Published on: September 20, 2018
[McCune Albright syndrome - diffuse orbital involvement due to fibrous dysplasia: a case report]
Márcio Alberto Costanzi1, Antonio Augusto Velasco e Cruz
1Departamento de Oftalmologia, Otorrinolaringologia e Cirurgia de Cabeça e Pescoço, Faculdade de Medicina, Universidade de São Paulo, Ribeirão Preto, SP, Brasil. marciocostanzi@bol.com.br
Abstract:
Fibrous dysplasia is a benign, slowly progressive bone disorder, in which normal bone is replaced by fibrous tissue. It is called McCune Albright syndrome when associated with skin hyperpigmentation and endocrinological disorders. We report a rare case of McCune Albright syndrome in a boy, who presented bilateral and diffuse involvement of orbits but few external craniofacial distortions.
