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Published on: February 11, 2022
Isolated atrioventricular discordance: surgical experience.
Rajesh Sharma1, Ashutosh Marwah, Sejal Shah
1Departments of Pediatric Cardiology and Cardiovascular Surgery, Narayana Hrudayalaya Institute of Medical Sciences, Bangalore, India. rsharmacvs@hotmail.com
The Annals of Thoracic Surgery
|March 22, 2008
Summary
This study shows that surgical repair of isolated ventricular inversion, a rare congenital heart defect, can be successful in most children. Early outcomes are promising, with survivors doing well after treatment for this complex cyanotic heart disease.
Area of Science:
- Pediatric Cardiology
- Congenital Heart Surgery
- Cardiac Anatomy
Background:
- Isolated ventricular inversion is an extremely rare cyanotic congenital heart disease.
- It presents similarly to D-transposition of great arteries, requiring intracardiac or extracardiac mixing for survival.
- Published literature is limited due to the anomaly's rarity.
Purpose of the Study:
- To review surgical experience with isolated ventricular inversion.
- To evaluate the outcomes of surgical repair in a cohort of affected children.
Main Methods:
- Surgical repair was performed on five children (aged 6 days to 22 months) with isolated ventricular inversion.
- Procedures included patch closure of interventricular communications, patent ductus arteriosus ligation, and modified Senning's or Mustard-type repairs.
- One patient required concomitant mitral valve repair.
Main Results:
- One early death occurred.
- Two patients developed complete heart block, with one requiring a permanent pacemaker.
- All surviving patients are doing well at a mean follow-up of 18 months.
Conclusions:
- Surgical repair of isolated atrioventricular discordance is achievable in the majority of patients.
- This complex anomaly can be managed successfully with appropriate surgical intervention.
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