Melanotic neuroectodermal tumour of infancy. A case report

Melanotic neuroectodermal tumour of infancy is a rare neoplasm of neural crest origin, predominantly affecting the anterior maxilla of infants. Treatment generally consists of surgical excision. Long-term follow-up is important since recurrence and malignant transformation have been reported. The literature about melanotic neuroectodermal tumour of infancy is reviewed and a case occurring in a 4-month old infant is presented.