Related Experiment Video
Updated: Jul 4, 2026
Surgical Treatment of an Endolymphatic Sac Tumor
Published on: May 26, 2023
Chiari I malformation presenting with hearing loss: surgical treatment and literature review
Gregory G Heuer1, Brandon Gabel, Paul S Lemberg
1Division of Neurosurgery, Children's Hospital of Philadelphia, Wood Center, 6th Floor, 34th and Civic Center Blvd, Philadelphia, PA 19104, USA.
Objects:
Chiari I malformations can present with a number of clinical signs and symptoms.
Methods:
We present a case of an 11-year-old girl that presented with significant sensorineural hearing loss as her only Chiari-related symptom. The patient had four audiograms that all demonstrated progressive bilateral hearing loss between 10 and 30 dB. On magnetic resonance scan, the patient was found to have a Chiari I malformation. The patient had 9 mm of tonsillar herniation but no syrinx or hydrocephalus was present. On exam, the patient did not exhibit any other symptoms of her Chiari malformation or cranial nerve abnormalities other than sensorineural hearing loss. The patient underwent a suboccipital craniotomy, C1 laminectomy, and duraplasty. The patient noted a subjective improvement in hearing and an audiogram performed at 3 months postoperatively demonstrated normal hearing bilaterally.
Conclusions:
Sensorineural hearing loss may be caused by Chiari I malformations. This symptom may improve following decompression.
More Related Videos
06:59Intrathecal Application of a Fluorescent Dye for the Identification of Cerebrospinal Fluid Leaks in Cochlear Malformation
Published on: February 29, 2020
03:49Enhanced Cochlear Coverage and Hearing Preservation in High-Frequency Hearing Loss via Electric Acoustic Stimulation with Longer Electrode
Published on: October 11, 2024