Supernumerary nipples in association with Hailey-Hailey disease in a Tunisian family

R Benmously-Mlika1, S Deghais, M Bchetnia

  • 1Dermatology Department, Habib Thameur Hospital, Tunis, Tunisia. rym.benmously@rns.tn

Supernumerary nipples (SNs) or polythelia are developmental abnormalities of breast tissue. They are located along the embryonic mammary lines. Polythelia usually occurs as a sporadic abnormality, although familial aggregation has been occasionally reported. Hailey-Hailey disease is a rare autosomal genodermatosis characterized by disturbed keratinocyte adhesion. These cutaneous disorders have been described in correlation with many other abnormalities. We report here the association of Hailey-Hailey disease and supernumerary nipples in a Northern Tunisian family. To our knowledge, this is the first report of such a clinical association.

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