Related Experiment Videos
[Hearts with double inlet ventricle. Morphological aspects in 20 cases]
V D Aiello1, F A Gomes, D C Monteiro
1Instituto do Coração do Hospital das Clínicas e Departamento de Patologia da FMUSP, São Paulo.
Arquivos Brasileiros De Cardiologia
|January 1, 1991
Summary
This study analyzed hearts with double inlet ventricle (DIV), revealing common anatomical variations and associated lesions. Early attention to obstructive pulmonary lesions in atrial isomerism is crucial for surgical palliation.
Area of Science:
- Congenital heart disease research
- Cardiac morphology and anatomy
- Pediatric cardiology
Context:
- Double inlet ventricle (DIV) presents complex anatomical challenges.
- Understanding anatomical variations is key for effective surgical strategies.
- Pathological analysis provides insights into congenital heart defects.
Purpose:
- To determine common anatomical presentations of double inlet ventricle (DIV).
- To identify associated cardiac lesions in DIV.
- To inform surgical palliation and correction strategies for DIV.
Summary:
- Analysis of 20 hearts with DIV revealed varied atrial arrangements (usual, right isomerism, left isomerism).
- Ventriculoarterial connections were discordant, concordant, or double outlet type.
- Associated lesions included obstructive pulmonary lesions (common in atrial isomerism), atrioventricular valve stenosis/straddling, and aortic coarctation.
Impact:
- Findings guide surgical planning for double inlet ventricle (DIV).
- Highlights the need for early intervention for obstructive pulmonary lesions in atrial isomerism.
- Informs management of atrioventricular valve dysfunction and aortic coarctation in DIV patients.