Sturge-Weber-Dimitri disease? In association with an astrocytoma
A Mahmood1, M Dujovny, J L Chason
1Henry Ford Neurosurgical Institute, Department of Neurological Surgery, Henry Ford Hospital Detroit, Michigan.
Acta Neurochirurgica
|January 1, 1991
Summary
This case study highlights a patient with Sturge-Weber-Dimitri disease (SWDD) who developed an astrocytoma, a rare occurrence, especially without typical facial portwine lesions. The association is likely coincidental.
Area of Science:
- Neurology
- Oncology
- Genetics
Background:
- Sturge-Weber-Dimitri disease (SWDD) is a rare neurocutaneous disorder.
- Typical SWDD involves portwine stains, epilepsy, and neurological deficits.
- Cortical calcification is a hallmark of SWDD.


