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Capsule endoscopy findings in congenital afibrinogenemia-associated angiopathy
P Katsinelos1, T Vasiliadis, K Soufleris
1Department of Endoscopy and Motility Unit, Central Hospital, Thessaloniki, Greece. papazio@med.auth.gr
VASA. Zeitschrift Fur Gefasskrankheiten
|November 13, 2008
Abstract:
Congenital afibrinogenemia is a rare genetic disorder characterized by the complete absence of functional fibrinogen. We report a 22-year-old female who developed nephrogenic arterial hypertension and intestinal ischemia due to congenital afibrinogenemia-associated angiopathy of large abdominal arteries. We describe, for the first time, the capsule findings and discuss the pathophysiology of this unusual condition.