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Neuro-rehabilitation Approach for Sudden Sensorineural Hearing Loss
Published on: January 25, 2016
Cochlear implant patients with superficial siderosis
Sarah A Sydlowski1, Michael J Cevette, Jon Shallop
1Mayo Clinic Arizona, Department of Audiology, 13400 East Shea Boulevard, Scottsdale, AZ 85259, USA. sarah.sydlowski@gallaudet.edu
Journal of the American Academy of Audiology
|July 15, 2009
Summary
Superficial siderosis of the central nervous system (SSCN) causes progressive hearing loss, but cochlear implantation (CI) may still be a viable option for patients. Careful audiological evaluation and counseling are crucial for managing expectations.
Area of Science:
- Neuroscience
- Otolaryngology
- Medical Diagnostics
Background:
- Superficial siderosis of the central nervous system (SSCN) is a rare, progressive disorder.
- It is increasingly diagnosed and characterized by sensorineural hearing loss, often exceeding hearing aid capabilities.
- The retrocochlear nature of SSCN hearing loss presents unique challenges.
Purpose of the Study:
- To review challenges for cochlear implant (CI) candidates with SSCN.
- To analyze performance trends following cochlear implantation in SSCN patients.
Main Methods:
- Retrospective analysis of seven cochlear implant candidates with SSCN.
- Detailed review of symptoms, audiologic presentation, and clinical issues.
Main Results:
- Cochlear implantation can be a viable treatment option for SSCN patients.
- Despite the retrocochlear hearing loss component, positive outcomes are possible.
Conclusions:
- Audiologists must be aware of SSCN and its implications for CI.
- Thorough case history, expanded testing, and adjusted counseling are essential for successful CI outcomes in SSCN patients.