[Congenital coronary fistula. Clinical presentation in 7 cases and literature review]
Alfa Larissa Nava-Oliva1, Felipe David-Gómez, Arturo Martínez-Sánchez
1Servicio de Cardiopatías Congénitas, Hospital de Cardiología, Centro Médico Nacional Siglo XXI (CMN Siglo XXI), Instituto Mexicano del Seguro Social, México, D.F. México.
Insights
Congenital coronary artery fistulas present differently in children and adults. Coronary angiography is key for diagnosis, and surgical treatment offers low risks for these uncommon cardiac anomalies.
Area of Science:
- Cardiology
- Pediatric Cardiology
- Adult Congenital Heart Disease
Background:
- Congenital coronary artery fistulas are rare cardiac anomalies.
- These fistulas can mimic various cardiac conditions.
- Clinical presentations differ significantly between pediatric and adult patients.
Observation:
- A study reviewed 7 cases of coronary artery fistulas diagnosed via selective coronariography between 2000 and 2007.
- Four pediatric cases (mean age 6.5 years) and three adult cases (mean age 25.6 years) were analyzed.
- Fistula origins and terminations varied, with different patterns observed in children versus adults.
Findings:
- In children, fistulas originated from the left coronary artery (3 cases) or right coronary artery (1 case).
- In adults, all fistulas originated from the right ventricle.
- Successful surgical repair was achieved in two children, with long-term asymptomatic outcomes. One adult patient developed a myocardial infarction post-surgery.
Implications:
- Clinical and hemodynamic features of coronary artery fistulas are age-dependent.
- Coronary angiography remains the gold standard for diagnosing these anomalies.
- Surgical intervention for coronary artery fistulas is associated with low mortality and morbidity rates.
Unlabelled:
Congenital coronary artery fistulas are uncommon anomalies, however themselves may resemble the whole spectrum of cardiac manifestations. Clinical presentations vary considerably from adults to children.
Material And Methods:
patients with coronary artery fistula diagnosed by selective coronariography in the period from 2000 to 2007 were included.
Results:
7 cases were found, 4 children, mean age 6.5 years, and 3 adults, mean age 25.6 years. The fistulae originate from the left coronary artery in 3 children, 2 connect to the pulmonary artery an one to the right atrium, in one child the fistula originated from the right coronary artery and terminated at the right ventricle. In the 3 adult patients, the fistula originated from the right ventricle, two connected to the right ventricle and one to the coronary sinus. Two children were operated on successfully and are asymptomatic 1 and 4 years later. In an adult patient with surgical ligation was performed, 4 weeks later developed an uncomplicated myocardial infarction. We reviewed the literature available and were compared with our cases.
Conclusions:
The clinical manifestations and hemodynamic features differ in childhood and adulthood. Coronary angiography is the primary diagnostic tool. Surgical treatment has low mortality and morbidity.
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