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Congenital tufted angioma with persistent low-grade coagulopathy
R Ramesh1, B De Silva, D J Atherton
1Department of Dermatology, Luton and Dunstable Hospital, Luton, UK. raakhee.ramesh@gmail.com
Clinical and Experimental Dermatology
|September 26, 2009
Summary
A tufted angioma in a female infant caused a coagulopathy. Conservative observation was chosen due to uncertain risk of Kasabach-Merritt phenomenon, and this approach proved successful.
Area of Science:
- Pediatric Hematology
- Vascular Anomalies
Background:
- Tufted angiomas are rare vascular tumors.
- Infants with tufted angiomas can develop coagulopathy.
- Kasabach-Merritt phenomenon is a severe complication associated with vascular tumors.
Observation:
- A female infant presented with a tufted angioma.
- The infant developed a coagulopathy characterized by prolonged bleeding time.
- The clinical challenge was to accurately assess the risk of progression to Kasabach-Merritt phenomenon.
Findings:
- A conservative management strategy involving observation was selected.
- This conservative approach was deemed appropriate given the assessed risk.
- The chosen management strategy led to a favorable outcome.
Implications:
- This case highlights the importance of careful risk assessment in managing infants with tufted angiomas.
- Conservative management may be a viable option when the risk of severe complications is uncertain.
- Further research into predicting and managing coagulopathy in vascular anomalies is warranted.
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