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Basilar impression in osteogenesis imperfecta tarda. Case report.
M Kurimoto1, S Ohara, A Takaku
1Department of Neurosurgery, Yao Tokushukai Hospital, Osaka, Japan.
Journal of Neurosurgery
|January 1, 1991
Summary
This case study shows that posterior fossa decompression and fusion can successfully treat basilar impression in patients with osteogenesis imperfecta tarda, alleviating symptoms like hemifacial spasm and brain-stem compression.
Area of Science:
- Neurology
- Neurosurgery
- Genetics
Background:
- Basilar impression is a complex skull base abnormality.
- Osteogenesis imperfecta tarda (OI Tarda) can lead to basilar impression.
- OI Tarda-associated basilar impression may cause neurological deficits.