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Updated: Jun 17, 2026

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Optic Nerve Sheath Point of Care Ultrasound: Image Acquisition
Published on: August 18, 2023
A primary optic nerve sheath chordoid meningioma
Aliasgar V Moiyadi1, Epari Sridhar, Tejpal Gupta
1Neurosurgery Services, Department of Surgical Oncology, Room 48, Main Building, Tata Memorial Hospital, E Borges Road, Parel, Mumbai 400 012, India. aliasgar.moiyadi@gmail.com
Summary
Optic nerve sheath meningiomas (ONM) are rare tumors. This case report details an unusual chordoid meningioma variant presenting as an exophytic mass, highlighting its rarity in primary ONM.
Area of Science:
- Ophthalmology
- Neuropathology
- Oncology
Background:
- Primary optic nerve sheath meningiomas (ONM) are rare, typically World Health Organization Grade I tumors.
- Surgical removal is often challenging due to the tumor's proximity to the optic nerve sheath.
- Chordoid meningiomas are an infrequent subtype, exceptionally rare in primary ONM.
Observation:
- A 36-year-old woman presented with painless proptosis and preserved visual acuity.
- An exophytic intraconal mass was identified and surgically excised.
- Histopathological examination confirmed the diagnosis of chordoid meningioma.
Findings:
- The excised mass was confirmed as a chordoid meningioma, a rare variant of ONM.
- This represents one of the few reported cases of primary chordoid meningioma of the optic nerve sheath.
- The case adds to the limited literature on this specific tumor type.
Implications:
- This case underscores the importance of considering rare meningioma variants in the differential diagnosis of optic nerve sheath masses.
- Further research into the behavior and management of chordoid meningiomas is warranted.
- Accurate histopathological diagnosis is crucial for appropriate patient management and prognosis.
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