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Cystic fibrosis and transition to adult medical care

Lisa K Tuchman1, Lisa A Schwartz, Gregory S Sawicki

  • 1Division of Adolescent and Young Adult Medicine, Center for Clinical and Community Research, Children's National Medical Center, George Washington University School of Medicine and Health Sciences, Washington, DC, USA. ltuchman@cnmc.org

Pediatrics
|February 24, 2010
PubMed

Insights

Transitioning young adults with cystic fibrosis (CF) from pediatric to adult care is crucial. Defining and measuring successful outcomes for this transition remains a challenge for healthcare providers.

Area of Science:

  • Pediatric Medicine
  • Pulmonology
  • Healthcare Management

Background:

  • Increasing lifespan of cystic fibrosis (CF) patients necessitates specialized adult care.
  • Over half of CF patients are adults, highlighting the need for effective transition strategies.
  • The Cystic Fibrosis Foundation has initiated programs to support adult CF care.

Purpose of the Study:

  • To review the challenges in healthcare transition for young adults with CF.
  • To provide context for designing and evaluating successful transition processes.
  • To discuss implications for all youth with special healthcare needs.

Main Methods:

  • State-of-the-art literature review.
  • Analysis of current transition practices and outcomes in CF care.
  • Examination of developmental needs for self-management in young adults.

Main Results:

  • The optimal facilitation and outcome measurement for CF healthcare transition are unclear.
  • Many young adults with CF remain in pediatric care or transfer unprepared.
  • Existing initiatives address provider training and program establishment but not outcome definition.

Conclusions:

  • Effective healthcare transition for young adults with CF requires further research and clear outcome metrics.
  • Developmental readiness and health system support are key to successful self-management transfer.
  • Lessons learned from CF transition can inform care for other special healthcare needs populations.

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