Foster Kennedy Syndrome in a Case with Retinitis Pigmentosa

A 57-year-old woman suffering from long-term visual disturbance due to retinitis pigmentosa noted an even more severe deterioration of her left vision for several months. On ophthalmologic examination, her vision was 1/60 in the right eye and light perception (LP) in the left eye. An RAPD sign was noted in her left eye. Bilateral fundus revealed the typical appearance of severe retinitis pigmentosa. The optic disc of her right eye was markedly swollen, whereas that of the left eye was pale. Under the impression of the Foster Kennedy syndrome, a magnetic resonance imaging (MRI) study was arranged revealing a well-encapsulated round mass with a contrast enhancement of about 4.45 cm in diameter located in the left frontal lobe. The patient might have ignored the visual disturbance in her left eye caused by tumor compression because of her illness of retinitis pigmentosa, which had caused her visual disturbance since childhood.