Noninvasive ventilation in cystic fibrosis

Brigitte Fauroux1

  • 1AP-HP, Hopital Armand Trousseau, Pediatric Pulmonary Department, Research unit INSERM UMR 5-938, National Reference Centre for Rare Lung Diseases, Pierre et Marie Curie-Paris University, 28 Avenue du Docteur Arnold Netter, Paris F-75012, France. brigitte.fauroux@trs.aphp.fr

Summary

Noninvasive positive pressure ventilation (NPPV) can improve breathing in cystic fibrosis patients by reducing respiratory muscle load and enhancing gas exchange. Further research is needed to confirm long-term benefits for survival and quality of life.

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