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Updated: Jun 12, 2026

Three-Dimensional Printing of a Complex Aortic Anomaly
Published on: November 1, 2018
Polysplenia/heterotaxy syndrome associated with aortic coarctation and multiple venous anomalies: multidetector
Aysegul Karadeniz1, Aslihan Semiz Oysu, Sinan Sahin
1Department of Radiology, Dr. Siyami Ersek Thoracic and Cardiovascular Surgery Training and Research Hospital, Istanbul, Turkey.
Abstract:
Polysplenia/heterotaxy syndrome is a rare condition involving multiple gastrointestinal, vascular, and cardiac malformations. We present a previously unreported association of aortic coarctation, double superior vena cava, a left-hand side inferior vena cava with hemiazygos vein continuation and a right retroaortic renal vein with polysplenia/heterotaxy syndrome. Multidetector computed tomography with multiplanar reconstruction images were useful in the detection of these abnormalities.
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