Malignant fibrohistocytoma of the maxilla presenting with endodotically involved teeth

It is well established that a periapical lesion may be the first presenting form of more serious disease. A case of malignant fibrohistocytoma has been presented. It is of special interest because of the rarity of the disease, especially in the jaws, and because it presented as periapical disease associated with nonvital teeth. The case emphasizes the value of routine histopathologic examination of tissue and the need for maintaining a high "index of suspicion" when dealing with clinically atypical behavior. The value of consultation with an oral pathologist has also been stressed.