Malignant peripheral nerve sheath tumor of the infratemporal fossa

Malignant peripheral nerve sheath tumor is a rare pathologic lesion in a patient without neurofibromatosis diseases. The patient is a 36-year-old man without any congenital or systemic diseases who presented with a firm and painful mass on the left preauricular and temporomandibular joint area with paresthesia of temporal region. Clinical diagnosis of this tumor was made with delay owing to the lack of initial sign and symptoms and its location.