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Updated: Jun 12, 2026
05:17
Percutaneous Endoscopic Unilateral-Approach Bilateral Decompression for Lumbar Spinal Stenosis
Published on: February 9, 2024
Bilateral Lhermitte-Duclos disease.
Mustafa Bozbuga1, Ilker Gulec, Hikmet Turan Suslu
12nd Department of Neurosurgery, Lutfi Kirdar Kartal Education and Research Hospital, Istanbul, Turkey.
Neurology India
|May 29, 2010
Summary
Lhermitte-Duclos disease (LDD) typically presents unilaterally. This report details a rare case of LDD with bilateral cerebellar lesions successfully managed with surgical resection.
Area of Science:
- Neurology
- Neurosurgery
- Pathology
Background:
- Lhermitte-Duclos disease (LDD) is characterized by cerebellar granule cell layer hypertrophy.
- It typically manifests as a unilateral cerebellar or vermian lesion.
Observation:
- A 28-year-old woman presented with a year of progressive headache, nausea, vomiting, and blurred vision.
- Neurologic examination revealed bilateral papilledema, dysmetria, and dysdiadochokinesia.
- Imaging showed bilateral cerebellar hemisphere lesions causing posterior fossa mass effect, hydrocephalus, and Chiari type I malformation.
Findings:
- Surgical management involved a suboccipital-retrosigmoid approach with complete resection of the left intracerebellar mass.
- Postoperative symptoms of elevated intracranial pressure resolved rapidly.
Implications:
- This case highlights the possibility of bilateral LDD and successful surgical intervention.
- Complete resection can effectively alleviate symptoms associated with mass effect and hydrocephalus in LDD.
- Further research into the pathogenesis and varied presentations of LDD is warranted.
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