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Cochlear Implantation in the Guinea Pig
Published on: June 15, 2018
Cochlear implantation in pontine tegmental cap dysplasia
Andrea Bacciu1, Francesca Ormitti, Enrico Pasanisi
1Department of Otolaryngology, University of Parma, Via Gramsci 14, 43100 Parma, Italy. andreabacciu@yahoo.it
International Journal of Pediatric Otorhinolaryngology
|July 15, 2010
Summary
Pontine tegmental cap dysplasia (PTCD) is a rare brain malformation. Cochlear implantation in a child with PTCD significantly improved speech perception and intelligibility, enhancing quality of life.
Area of Science:
- Neuroscience
- Genetics
- Pediatrics
Background:
- Pontine tegmental cap dysplasia (PTCD) is an extremely rare congenital brain malformation affecting the brainstem and cerebellum.
- Key features include pontine hypoplasia, vermian hypoplasia, absent cerebellar peduncles, and cranial neuropathies.
- Sensorineural hearing loss is a near-universal clinical manifestation of PTCD.
