Association of three different congenital malformations in a same pulmonary lobe in a 5-year-old girl

A Carsin1, L Mely, M A Chrestian

  • 1Unité de Médecine Infantile, CHU Timone-Enfants and CNRS URMITE 6234, Marseille Cedex 05, France.

Pediatric Pulmonology
|July 24, 2010
PubMed

Insights

A child had persistent lung abnormalities after pneumonia, revealing a rare complex congenital pulmonary malformation. This case suggests a shared origin for these lung development issues.

Area of Science:

  • Pediatric Pulmonology
  • Thoracic Surgery
  • Developmental Biology

Background:

  • Congenital pulmonary airway malformation (CPAM) and intralobar sequestration (ILS) are rare lung malformations.
  • Bronchogenic cysts are also uncommon congenital lung abnormalities.
  • Co-occurrence of these malformations within a single lobe is exceptionally rare.

Related Concept Videos

Gross Anatomy of the Lungs01:17

Gross Anatomy of the Lungs

The lungs are a pair of vital organs connected to the trachea via the left and right bronchi. The base of these organs meets the dome-shaped muscle known as the diaphragm. Encased by the pleurae, the lungs contact the mediastinum. The right lung is shorter yet wider, and has a larger volume than the left lung. The left lung has an indentation known as the cardiac notch. The superior region of the lungs is referred to as the apex, whereas the base is the lower region near the diaphragm. The...
Pulmonary Hypertension: Classification and Pathogenesis01:30

Pulmonary Hypertension: Classification and Pathogenesis

Pulmonary hypertension (PH) is a severe health condition in which the mean pulmonary arterial pressure increases to 25 mmHg or more, even when the body is at rest. This high pressure in the blood vessels that transport blood from the heart to the lungs can cause various symptoms, including shortness of breath, can lead to right heart failure, and significantly affect the overall quality of life.
There are various classifications for PH, each relating to different underlying causes and also...