[Primary pulmonary hypertension in children]

The aetiology, pathogenesis, clinical manifestations and course of primary pulmonary hypertension are discussed in children, describing the diagnostic methods in this disease entity. In view of the suggestion that vasoconstriction plays an important role in the pathogenesis of this disease attention is called to the usefulness of pharmacological test done during cardiac catheterization. Such tests could indicate the direction of further therapeutic measures.