Sinus pericranii presenting with macrocephaly and mental retardation.
R B Kamble1, N K Venkataramana, L Naik
1Department of Radiology and Neurosurgery, BGS Global Hospital, Uttarahalli Road, Kengeri, Bangalore - 560 098, India.
Journal of Pediatric Neurosciences
|November 3, 2010
Summary
A rare case of sinus pericranii, a scalp vascular malformation, was found in a 2-year-old child. Imaging confirmed the diagnosis of this unusual condition.
Area of Science:
- Vascular Surgery
- Pediatric Radiology
- Neurosurgery
Background:
- Sinus pericranii is a rare congenital vascular malformation involving abnormal communication between intracranial venous sinuses and extracranial veins.
- It can present as a compressible scalp swelling, often associated with increased intracranial pressure or macrocephaly.
Observation:
- A 2-year-old female child presented with a compressible right parietal scalp swelling noted since 3 months of age.
- The child also exhibited macrocephaly, indicating a potentially larger head circumference than expected for age.
Findings:
- Diagnostic imaging, including magnetic resonance imaging (MRI) with venography and conventional angiography, confirmed the presence of right parietal sinus pericranii.
- The imaging delineated the abnormal vascular connection and its extent.
Implications:
- This case highlights the importance of considering sinus pericranii in the differential diagnosis of pediatric scalp masses and macrocephaly.
- Accurate diagnosis through advanced imaging is crucial for appropriate management and to rule out associated intracranial abnormalities.
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