Related Experiment Video
Updated: Jun 6, 2026
04:00
Laparoscopic Splenectomy with Pericardial Devascularization for Hypersplenism and Esophageal Variceal Hemorrhage Due to Portal Hypertension
Published on: November 15, 2024
Massive hemoperitoneum with splenic infarction in Evans syndrome
Eun Mi Ryu1, Soo Ah Im, Ho Jong Chun
1Department of Radiology, Seoul St. Mary's Hospital, The Catholic University of Korea, Republic of Korea.
Journal of Pediatric Hematology/Oncology
|November 20, 2010
Summary
Evans syndrome, a rare autoimmune disorder, can lead to severe complications. This case highlights splenic rupture and hemoperitoneum, a rare but critical event in pediatric patients.
Area of Science:
- Hematology
- Autoimmunology
- Pediatric Medicine
Background:
- Evans syndrome is a rare autoimmune hematologic disorder.
- It involves hemolytic anemia and immune thrombocytopenia.
- Complications typically include bleeding, rarely thrombosis.
Observation:
- An 18-month-old male with Evans syndrome presented with splenic infarction and rupture.
- This led to massive hemoperitoneum.
- Splenic artery embolization was performed.
Findings:
- This case demonstrates an extremely rare presentation of Evans syndrome.
- Splenic infarction and rupture are unusual complications.
- Successful splenic artery embolization was achieved.
Implications:
- Highlights the potential for severe vascular complications in Evans syndrome.
- Emphasizes the importance of prompt diagnosis and intervention.
- Informs management strategies for rare pediatric hematologic emergencies.
Related Concept Videos
01:24Esophageal Varices-I: Introduction
Esophageal varices are dilated, tortuous veins which are found mainly in the submucosa of the lower esophagus but which may also appear higher up or extend into the stomach. They develop due to increased pressure in the portal venous system, often as a result of liver cirrhosis. This condition scars and damages the liver, impeding normal blood flow through the portal vein. To compensate, blood seeks alternative pathways, forming fragile new vessels (varices) in the esophagus and stomach. These...
01:28Esophageal Varices-II: Clinical Features and Management
Esophageal varices often manifest as gastrointestinal bleeding episodes, presenting symptoms like hematemesis (vomiting of blood), hematochezia (passing fresh blood via the rectum), and melena (black, tarry stools). Other signs can include weight loss, anorexia, abdominal discomfort, jaundice, pruritus, altered mental status, and muscle cramps.
In the initial assessment, a thorough review of the patient's medical history is vital to identify risk factors such as liver disease, alcohol abuse, or...
In the initial assessment, a thorough review of the patient's medical history is vital to identify risk factors such as liver disease, alcohol abuse, or...
01:29Hemorrhagic Stroke ll: Pathophysiology
A hemorrhagic stroke develops when a cerebral blood vessel ruptures, allowing blood to escape into the surrounding brain tissue, as in intracerebral hemorrhage (ICH), or into the subarachnoid space, as in subarachnoid hemorrhage (SAH). Because the skull is a rigid compartment, the sudden presence of extravascular blood rapidly increases intracranial pressure and compresses adjacent neural structures, leading to immediate tissue injury and impaired cerebral perfusion.Mass Effect and Primary...
01:29Pulmonary Embolism II: Diagnostic Studies and Interprofessional Care
Diagnosing Pulmonary EmbolismDiagnosing pulmonary embolism (PE) involves clinical assessment and advanced imaging tests. The preferred diagnostic tool is the spiral (helical) CT scan or CT angiography (CTA), which uses intravenous contrast media to visualize the pulmonary vasculature and identify emboli.A ventilation-perfusion (V/Q) scan is an alternative for patients unable to receive contrast media. This scan includes both perfusion and ventilation scanning. Perfusion scanning involves...
01:22Portal Hypertension
Portal hypertension is an increase in blood pressure within the portal venous system. Normally, this pressure is less than 5 mmHg. It is considered clinically significant when it rises above 10 mmHg. At this threshold, complications from altered blood flow and venous congestion emerge.EtiologyPortal hypertension arises from conditions that impede blood flow through the liver. The most common cause is cirrhosis, in which chronic liver injury leads to fibrotic scarring. This fibrosis narrows or...