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Updated: Jun 6, 2026
06:32
Coronoid-Temporalis Pedicled Flap for Orbital Floor Defect Reconstruction
Published on: December 5, 2025
Congenital cranio-orbital myofibroma
Bülent Yazici1, Ayse Dolar Bilge, Zeynep Yazici
1Department of Ophthalmology, Uludag University, Bursa, Turkey. byazici@uludag.edu.tr
Ophthalmic Plastic and Reconstructive Surgery
|November 20, 2010
Summary
A rare infantile myofibroma caused severe proptosis in a newborn. This cranio-orbital tumor, though challenging, can be managed with tumor debulking via orbitotomy.
Area of Science:
- Pediatric Oncology
- Ophthalmology
- Neurosurgery
Background:
- Congenital proptosis in newborns necessitates prompt diagnosis and management.
- Cranio-orbital tumors are rare but present significant diagnostic and therapeutic challenges.
Observation:
- A 1-day-old female infant presented with severe left proptosis.
- Imaging revealed a cranial mass involving both orbits and ethmoid sinuses.
Findings:
- Histologic examination confirmed infantile myofibroma.
- The tumor was confined to the cranio-orbital region without systemic involvement.
Implications:
- Infantile myofibroma should be considered in the differential diagnosis of congenital proptosis and cranio-orbital masses.
- Lateral orbitotomy is a viable approach for tumor debulking in such cases.
- Despite surgical intervention, the patient experienced a fatal respiratory arrest post-intracranial surgery.
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