[Systemic scleroderma (apropos of a case with dominant pulmonary manifestations)]

A case of systemic sclerodermy mainly affecting the lungs is presented. For a long time the diagnostic was incorrect. The case is all the more interesting since the patient had worked in iron mines and unproved pneumoconiosis had been diagnosed. Treatment basically with corticotherapy and oxygenotherapy, with D-penicillamine added, produced a satisfactory outcome to the attack and definite improvements in the cutaneous lesions.