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[Exocrine pancreas diseases in children]
1Unité de gastro-entérologie et nutrition, Hôpital d'Enfants de la Timone, Marseille, France.
Summary
Pediatric exocrine pancreatic disorders, excluding cystic fibrosis, are rare but diverse. This review covers their pathogenesis, clinical features, and recent insights into cystic fibrosis-related pancreatic conditions.
Area of Science:
- Pediatric Gastroenterology
- Pancreatic Diseases
Context:
- Exocrine pancreatic disorders are infrequent in pediatric populations.
- Cystic fibrosis is a notable exception with significant pancreatic involvement.
Purpose:
- To survey diverse pediatric exocrine pancreatic diseases.
- To discuss recent theories on pancreatic involvement in cystic fibrosis.
Summary:
- Reviews the varied pathogenesis and clinical manifestations of pancreatic diseases in children.
- Highlights current understanding of cystic fibrosis and its impact on the exocrine pancreas.
Impact:
- Provides a comprehensive overview for clinicians and researchers in pediatric gastroenterology.
- Enhances understanding of rare pancreatic conditions and cystic fibrosis management.