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[Mesenteric fibromatosis in infants. A case]
Y Laborde1, J Saint-Martin, F Etcharry
1Service de chirurgie digestive, CHG, Pau, France.
Pediatrie
|January 1, 1990
Insights
Mesenteric fibromatosis, a rare condition, was successfully treated in a 5-month-old infant via surgical excision. The infant showed no recurrence of the desmoid tumor after 30 months, indicating a favorable clinical outcome.
Area of Science:
- Pediatric Surgery
- Surgical Pathology
- Pediatric Oncology
Background:
- Mesenteric fibromatosis (desmoid tumor) is a rare, locally aggressive soft tissue neoplasm.
- It presents a diagnostic challenge in infants due to its rarity and potential for misdiagnosis.
- Understanding its clinical and histological features is crucial for timely intervention.
Observation:
- A case of mesenteric fibromatosis in a 5-month-old infant is presented.
- The infant underwent successful surgical excision of the tumor.
- Post-operative follow-up revealed no signs of recurrence for 30 months.
Findings:
- Surgical excision is an effective treatment modality for pediatric mesenteric fibromatosis.
- The clinical course following complete resection was favorable.
- Histological examination aids in differentiating desmoid tumors from other intra-abdominal masses.
Implications:
- Early diagnosis and surgical management can lead to excellent outcomes in infants with mesenteric fibromatosis.
- This case highlights the importance of considering desmoid tumors in the differential diagnosis of abdominal masses in children.
- Further research into the etiology and optimal management strategies for pediatric desmoid tumors is warranted.
Abstract:
The authors report on a case of mesenteric fibromatosis in a 5 month-old infant. Surgical excision was available and the clinical course was good, without recurrence after 30 months. Clinical and histological features of mesenteric desmoïd tumor in children are discussed and diagnostic difficulties are examined in depth.