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[Mesenteric fibromatosis in infants. A case].
Y Laborde1, J Saint-Martin, F Etcharry
1Service de chirurgie digestive, CHG, Pau, France.
Pediatrie
|January 1, 1990
Summary
Mesenteric fibromatosis, a rare condition, was successfully treated in a 5-month-old infant via surgical excision. The infant showed no recurrence of the desmoid tumor after 30 months, indicating a favorable clinical outcome.
Area of Science:
- Pediatric Surgery
- Surgical Pathology
- Pediatric Oncology
Background:
- Mesenteric fibromatosis (desmoid tumor) is a rare, locally aggressive soft tissue neoplasm.
- It presents a diagnostic challenge in infants due to its rarity and potential for misdiagnosis.
- Understanding its clinical and histological features is crucial for timely intervention.
Observation:
- A case of mesenteric fibromatosis in a 5-month-old infant is presented.
- The infant underwent successful surgical excision of the tumor.
- Post-operative follow-up revealed no signs of recurrence for 30 months.
Findings:
- Surgical excision is an effective treatment modality for pediatric mesenteric fibromatosis.
- The clinical course following complete resection was favorable.
- Histological examination aids in differentiating desmoid tumors from other intra-abdominal masses.
Implications:
- Early diagnosis and surgical management can lead to excellent outcomes in infants with mesenteric fibromatosis.
- This case highlights the importance of considering desmoid tumors in the differential diagnosis of abdominal masses in children.
- Further research into the etiology and optimal management strategies for pediatric desmoid tumors is warranted.